Benign metastasizing leiomyoma (BML) is an extremely rare condition that occurs in women of all ages. However, it most commonly occurs in women aged 30-75, and particularly among women of late childbearing age.1 First reported by Steiner in 1939, BML has been reported in the literature only a handful of times.2 BML occurs in women with a history of uterine leiomyoma (fibroids) followed by hysterectomy or myomectomy. It usually presents within 15 years of the initial diagnosis of uterine leiomyoma.3 Distant metastasis is common with lungs and lymph nodes being the most common sites of spread. Other sites of metastasis reported in the literature include the central nervous system, heart, skin, esophagus, skeletal muscles, bones, breasts, and trachea.1 Once diagnosed, BML follows a steady disease course with a mean prognosis of 96 months.4

We present an extremely rare case of BML with atypical organ involvement that has not been previously reported in the literature. In addition, our case was unique because of its unusual radiological appearance and rapid disease course, which has also been only scarcely reported in the literature.