Case Report

Kikuchi-Fujimoto Disease with Subsequent Meningoencephalitis Insights into Rare Complications – A Case Report

Murad Ali Khan
Arif Memorial Teaching Hospital, Lahore
Asma Kazi
Arif Memorial Teaching Hospital, Lahore
Muhammad Sohail
Arif Memorial Teaching Hospital, Lahore
Aisha Aziz
Arif Memorial Teaching Hospital, Lahore
Faisal Zarar
Faaiqa Saqlain

✉ Correspondence: Asma Kazi Email: docasmakazi@gmail.com

DOI https://doi.org/10.70302/jpsim.v5i3.2458
Volume: 5, Issue 3 Pages: 649–653 Published: 30 Aug 2024
Received: 03 Mar 2024 Accepted: 07 Aug 2024 Published Online: 30 Aug 2024

Abstract

Kikuchi-Fujimoto Disease (KFD) is a rare, benign, self-limiting condition primarily affecting young adults and is often misdiagnosed due to its nonspecific symptoms. We present a rare case of a 36-year-old man who presented with high-grade fever, cervical lymphadenopathy, and weight loss. Despite a comprehensive workup, involving imaging studies and laboratory investigations, the diagnosis remained elusive until a lymph node excisional biopsy confirmed the Kikuchi disease. The patient developed meningoencephalitis, a rare but severe complication of KFD, characterized by seizures and altered mental status.Supportive care including non-steroidal anti-inflammatory drugs, and corticosteroids are the mainstay of management. The patient was discharged with a good prognosis. This case highlights the diagnostic challenges and potential severe neurological complications of KFD, emphasizing the need for heightened awareness and vigilant follow-up.

How to Cite This Article

Khan MA, Kazi A, Sohail M, Aziz A, Zarar F, Saqlain F. Kikuchi-Fujimoto Disease with Subsequent Meningoencephalitis Insights into Rare Complications – A Case Report. J Pak Soc Intern Med. 2024;5(3):649–653. doi:10.70302/jpsim.v5i3.2458

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Conflict of Interest

All authors declare no competing interests.

Disclosed in accordance with ICMJE and COPE guidelines.

Funding

No specific funding was received for this research.

Funder information follows the Crossref Funder Registry standard.

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CC BY CC BY 4.0 This article is published under the Creative Commons Attribution 4.0 International License. May be shared and adapted with attribution. © 2024 Journal of Pakistan Society of Internal Medicine.
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