Case Report

Pulomonary Arterial Hypertension and Aneurysm in Patient with Marfan Syndrome

Tariq Waseem1
1Akhtar Saeed Medical & Dental College Lahore Pakistan
Aasma Riaz2
City Healthcare IIc, USA
Shahzad Latif1
1Akhtar Saeed Medical & Dental College Lahore Pakistan
Wafa Qaisar1
1Akhtar Saeed Medical & Dental College Lahore Pakistan
Hina Latif3
King Edward Medical University, Lahore

✉ Correspondence: Tariq Waseem Email: tariqwaseem.kemu@gmail.com

DOI https://doi.org/10.70302/jpsim.v1i1.2015
Volume: 1, Issue 1 Pages: 67–70 Published: 16 Dec 2020
Received: 03 Sep 2020 Accepted: 22 Oct 2020 Published Online: 16 Dec 2020

Abstract

Cardiovascular involvement in Marfan syndrome is considered major criteria for its diagnosis and typically includes mitral valve prolapse, aortic root dilatation and aortic dissection. Pulmonary arterial trunk involvement in Marfan syndrome has rarely been reported. We report a case of a young Pakistani male presenting with dyspnea and fever who had morphological features of Marfan syndrome. On chest X-ray a left hilar mass was reported. Echocardiography of the patient revealed dilatation of pulmonary artery and moderate pulmonary hypertension. An aneurysm involving pulmonary artery and its left main trunk was confirmed on CT chest with IV contrast and on cardiac catheterization. Aneurysm of pulmonary trunk should be considered in the differential diagnosis of mediastinal masses in patients having Marfan syndrome.

Keywords
Marfan's Syndrome Pulmonary Artery Aneurysm Pulmonary hypertension.

How to Cite This Article

Waseem T, Riaz A, Latif S, Qaisar W, Latif H. Pulomonary Arterial Hypertension and Aneurysm in Patient with Marfan Syndrome. J Pak Soc Intern Med. 2020;1(1):67–70. doi:10.70302/jpsim.v1i1.2015

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Conflict of Interest

All authors declare no competing interests.

Disclosed in accordance with ICMJE and COPE guidelines.

Funding

No specific funding was received for this research.

Funder information follows the Crossref Funder Registry standard.

References

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CC BY CC BY 4.0 This article is published under the Creative Commons Attribution 4.0 International License. May be shared and adapted with attribution. © 2020 Journal of Pakistan Society of Internal Medicine.
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